Acquired double-barrel oesophagus in epidermolysis bullosa dystrophica.

Epidermolysis bullosa of the oesophagus with oesophageal wed formation.

Marsden, R. A., Sambrook Gowar, F. J., MacDonald, A. F., and Main, R. A. (1974). Thorax, 29, 287-295. Epidermolysis buBosa of the oesophagus with oesophageal web formation. Four members of a family are described with epidermolysis bullosa dystrophica of probable autosomal recessive inheritance. They have shown the typical blistering of the skin and oral mucosa, usually present at birth, which o...

Management of oesophageal stenosis in epidermolysis bullosa dystrophica.

Seven patients with epidermolysis bullosa dystrophica and chronic and recurrent oesophageal lesions such as spasm, strictures, and complete occlusion were studied. Dysphagia could be cured with drugs if it was caused by bullae formation or spasm. If oesophageal strictures were present, endoscopy and bouginage with corticosteroid prophylaxis during the quiescent phase of the disease was a safe a...

Historical perspective on dystrophic epidermolysis bullosa

Dystrophic epidermolysis bullosa pruriginosa: the first report of a family in malaysia.

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Epidermolysis Bullosa: Experience from the Western Province of Saudi Arabia

Epidermolysis bullosa is a rare inherited bullous disease with unknown prevalence in most parts of the world. In Saudi Arabia the reported studies regarding epidermolysis bullosa are very limited. This paper presents the first study of epidermolysis bullosa cases from the Western province of Saudi Arabia. We studied 15 cases of inherited epidermolysis bullosa and classified the cases based on e...